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forme I
med. Dyskeratosis intrauterina (ichthyosis congenita gravis RIECKE); Ichthyosis congenita gravis (ichthyosis congenita gravis RIECKE); Ichthyosis fetalis (ichthyosis congenita gravis RIECKE); Keratoma malignum intrauterinum diffusa maligna sive fetalis diffusa (ichthyosis congenita gravis RIECKE)